Methylglutaric acid
Methylglutaric acid structure
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Common Name | Methylglutaric acid | ||
|---|---|---|---|---|
| CAS Number | 626-51-7 | Molecular Weight | 146.141 | |
| Density | 1.2±0.1 g/cm3 | Boiling Point | 332.7±0.0 °C at 760 mmHg | |
| Molecular Formula | C6H10O4 | Melting Point | 81-86 °C(lit.) | |
| MSDS | Chinese USA | Flash Point | 148.8±16.3 °C | |
| Symbol |
GHS07 |
Signal Word | Warning | |
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Age-related reference values for urinary organic acids in a healthy Turkish pediatric population.
Clin. Chem. 40(6) , 862-6, (1994) Organic acid concentrations were quantified by gas chromatography and the individual acids identified by mass spectrometry in urine specimens from a healthy Turkish pediatric population of ages 2 days to 16 years, subdivided into five age groups. We quantifie... |
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Metabolomic profiles delineate potential role for sarcosine in prostate cancer progression.
Nature 457(7231) , 910-4, (2009) Multiple, complex molecular events characterize cancer development and progression. Deciphering the molecular networks that distinguish organ-confined disease from metastatic disease may lead to the identification of critical biomarkers for cancer invasion an... |
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NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism.
NMR Biomed. 19(2) , 271-8, (2006) A diagnosis of 3-methylglutaconic aciduria type I (OMIM: 250950) based on elevated urinary excretion of 3-methylglutaconic acid (3MGA), 3-methylglutaric acid (3MG) and 3-hydroxyisovaleric acid (3HIVA) was made in a 61-year-old female patient presenting with l... |
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3-Methylglutaconyl-coenzyme-A hydratase deficiency: a new case.
J. Inherit. Metab. Dis. 15(3) , 363-6, (1992)
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Urinary organic acid screening in children with developmental language delay.
J. Inherit. Metab. Dis. 22(7) , 815-20, (1999) The prevalence of 3-methylglutaconic aciduria was evaluated among children with developmental language disorders. A urine specimen was obtained from 40 children referred for developmental language delay to the Tel-Aviv Child Development Center during 12/96-6/... |
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Multiple respiratory chain abnormalities associated with hypertrophic cardiomyopathy and 3-methylglutaconic aciduria.
Eur. J. Pediatr. 152(8) , 665-70, (1993) In a 4.5-month-old boy presenting with marked muscular hypotonia in the neonatal period, hepatomegaly, cardiac hypertrophy, recurrent hypoglycemia, metabolic acidosis, and secondary carnitine deficiency, there was a considerable urinary excretion of 3-methylg... |
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3-Methylglutaconic and 3-methylglutaric aciduria in a patient with suspected 3-methylglutaconyl-CoA hydratase deficiency.
Eur. J. Pediatr. 143(4) , 301-3, (1985) A girl suffering from marked muscular hypotonia, severe statomotor and mental retardation, bilateral optic atrophy with chorioretinal degeneration, convulsions and a moderate compensated metabolic acidosis is described. Screening for metabolic disorders revea... |
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3-hydroxy-3-methylglutaric, 3-methylglutaconic and 3-methylglutaric acids can be non-specific indicators of metabolic disease.
J. Inherit. Metab. Dis. 7 Suppl 2 , 117-8, (1984)
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Mitochondrial DNA depletion associated with partial complex II and IV deficiencies and 3-methylglutaconic aciduria.
J. Child Neurol. 16(2) , 136-8, (2001) We report a patient with mitochondrial DNA depletion, partial complex II and IV deficiencies, and 3-methylglutaconic aciduria. Complex II deficiency has not been previously observed in mitochondrial DNA depletion syndromes. The observation of 3-methylglutacon... |
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3-Methylglutaconyl-CoA hydratase deficiency: a new patient with speech retardation as the leading sign.
J. Inherit. Metab. Dis. 23(4) , 341-4, (2000)
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