Journal of Inherited Metabolic Disease 1981-01-01

Renal transport of aromatic acids in patients with phenylketonuria.

U Langenbeck, A Behbehani, H Luthe

Index: J. Inherit. Metab. Dis. 4(2) , 69-70, (1981)

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Abstract

Renal clearance of phenylpyruvic acid is maximal at a plasma concentration of 40-60 mumol/l. This concentration is obtained with plasma phenylalanine concentrations of 1.0-1.2 mmol/l, the threshold for separating classical phenylketonuria from phenylketonuria variants.