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(R)-β-羟基异丁酸钠

(R)-β-羟基异丁酸钠名称

[ CAS 号 ]:
1228078-57-6

[ 中文名 ]:
(R)-β-羟基异丁酸钠

[ 英文名 ]:
Sodium(R)-β-hydroxyisobutyrate

[英文别名 ]:

(R)-3-Hydroxy-2-methylpropionic acid sodium salt
R-HIBA
(R)-|A-Hydroxyisobutyric acid sodium salt
Sodium (R)-3-hydroxy-2-methylpropionate
Sodium (R)-|A-hydroxyisobutyrate

(R)-β-羟基异丁酸钠物理化学性质

[ 分子式 ]:
C₄H₇NaO₃

[ 分子量 ]:
126.08600

[ 精确质量 ]:
126.02900

[ PSA ]:
60.36000

[ 外观性状 ]:
白色粉末

[ 储存条件 ]:
2-8°C，密封，干燥

(R)-β-羟基异丁酸钠MSDS

详细MSDS(安全技术说明书)

(R)-β-羟基异丁酸钠安全信息

[ 危险品运输编码 ]:
NONH for all modes of transport

(R)-β-羟基异丁酸钠文献

Stereodifferentiation of 3-hydroxyisobutyric- and 3-aminoisobutyric acid in human urine by enantioselective multidimensional capillary gas chromatography-mass spectrometry.

Clin. Chim. Acta 292 , 93-105, (2000)

The chiral metabolites 3-hydroxyisobutyric acid (HIBA) and 3-aminoisobutyric acid (AIBA) are intermediates in the pathways of L-valine and thymine and play an important role in the diagnosis of the ve...

Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway.

J. Inherit. Metab. Dis. 35 , 5-12, (2012)

Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the val...

Mutations in the gene encoding 3-hydroxyisobutyryl-CoA hydrolase results in progressive infantile neurodegeneration.

Am. J. Hum. Genet. 80 , 195-199, (2007)

Only a single patient with 3-hydroxyisobutyryl-CoA hydrolase deficiency has been described in the literature, and the molecular basis of this inborn error of valine catabolism has remained unknown unt...

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