European Journal of Pediatrics 2010-01-01

Biochemical efficacy of N-carbamylglutamate in neonatal severe hyperammonaemia due to propionic acidaemia.

Bernd C Schwahn, Louisa Pieterse, W Michael Bisset, Peter G Galloway, Peter H Robinson

Index: Eur. J. Pediatr. 169(1) , 133-4, (2010)

Full Text: HTML

Abstract


Related Compounds

Related Articles:

Pricing of orphan drugs.

2009-02-07

[Lancet 373(9662) , 462, (2009)]

Effect of dietary arginine and N-carbamoylglutamate supplementation on reproduction and gene expression of eNOS, VEGFA and PlGF1 in placenta in late pregnancy of sows.

2012-06-01

[Anim. Reprod. Sci. 132(3-4) , 187-92, (2012)]

Oral N-carbamylglutamate supplementation increases protein synthesis in skeletal muscle of piglets.

2007-02-01

[J. Nutr. 137(2) , 315-9, (2007)]

N-carbamylglutamate markedly enhances ureagenesis in N-acetylglutamate deficiency and propionic acidemia as measured by isotopic incorporation and blood biomarkers.

2008-08-01

[Pediatr. Res. 64(2) , 213-7, (2008)]

Effects of dietary L-arginine or N-carbamylglutamate supplementation during late gestation of sows on the miR-15b/16, miR-221/222, VEGFA and eNOS expression in umbilical vein.

2012-06-01

[Amino Acids 42(6) , 2111-9, (2012)]

More Articles...